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Combination of targeted therapy and immune checkpoint blocker in a patient with xeroderma pigmentosum presenting an aggressive angiosarcoma and a recurrent non-resectable basal cell carcinoma

Published:April 23, 2021DOI:https://doi.org/10.1016/j.ejca.2021.03.022
      Xeroderma pigmentosum (XP) is an autosomal recessive disorder characterised by deficient nucleotide excision repair (NER) of ultraviolet-induced DNA damage resulting in an increased skin carcinogenesis [
      • Lehmann A.R.
      • et al.
      Xeroderma pigmentosum.
      ].
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